text: （六）补体缺陷（表17-17）表17-5补体缺陷注：AD为常染色体显性遗传，AR为常染色体隐性遗传，XL为X-连锁遗传广义的补体系统涉及一组血浆蛋白质，由两部分组成：①补体各活性成分C1～C9，B因子和甘露糖结合素（mannosebindinglectin，MBL）；②补体调节蛋白，C1抑制物，C4结合蛋白，D因子，I因子，备解素，H因子，腐败加速因子（decayacceleratingfactor，DAF，CD55）和保护因子（protectin，CD59）。
entities.entity: 补体缺陷
entities.label: dis
entities.entity: 补体缺陷
entities.label: dis
entities.entity: AD
entities.label: dis
entities.entity: 常染色体
entities.label: bod
entities.entity: AR
entities.label: dis
entities.entity: 常染色体
entities.label: bod
entities.entity: X-连锁
entities.label: bod
entities.entity: 血浆蛋白质
entities.label: bod
entities.entity: 补体
entities.label: bod
entities.entity: B因子
entities.label: bod
entities.entity: 甘露糖结合素
entities.label: bod
entities.entity: mannosebindinglectin
entities.label: bod
entities.entity: MBL
entities.label: bod
entities.entity: 补体调节蛋白
entities.label: bod
entities.entity: C1抑制物
entities.label: bod
entities.entity: C4结合蛋白
entities.label: bod
entities.entity: D因子
entities.label: bod
entities.entity: I因子
entities.label: bod
entities.entity: 备解素
entities.label: bod
entities.entity: H因子
entities.label: bod
entities.entity: 腐败加速因子
entities.label: bod
entities.entity: decayacceleratingfactor
entities.label: bod
entities.entity: DAF
entities.label: bod
entities.entity: CD55
entities.label: bod
entities.entity: 保护因子
entities.label: bod
entities.entity: protectin
entities.label: bod