translation.en: The clinical picture is characterised by progressive neurological symptoms and death, with a mean survival of about 14 months from the onset of symptoms.
translation.mt: L-istampa klinika hi kkaratterizzata minn sintomi progressivi newroloġiċi u l-mewt, b'sopravivenza fqira ta' madwar 14-il xahar mill-bidu tas-sintomi.